Uncombable hair syndrome This syndrome presents during infancy or childhood with “spun glass” hair. The hair is blond, grows slowly, and is extremely difficult.

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Erythematous maculopapular and urticarial edematous plaques are seen on the thighs (A). (B) in a patient 2 weeks after receiving Bactrim. Fever, arthralgia,

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Presentation transcript:

Uncombable hair syndrome This syndrome presents during infancy or childhood with “spun glass” hair. The hair is blond, grows slowly, and is extremely difficult to comb or manage. Subtle longitudinal grooves may be noted on light microscopy and are clearly seen with a scanning electron microscope. Autosomal dominant inheritance is seen in some cases, and the condition may improve as the patient grows older. Source: Disorders of Nails and Hair, Weinberg's Color Atlas of Pediatric Dermatology, 5e Citation: Prose NS, Kristal L. Weinberg's Color Atlas of Pediatric Dermatology, 5e; 2017 Available at: https://accesspediatrics.mhmedical.com/DownloadImage.aspx?image=/data/books/1913/weinderm5_ch29_f031.png&sec=138563461&BookID=1913&ChapterSecID=138563409&imagename= Accessed: November 10, 2017 Copyright © 2017 McGraw-Hill Education. All rights reserved