A case of bulbospinal muscular atrophy with large fasciculation manifesting as spinal myoclonus Manabu Inoue, Yasuhiro Kojima, Masutaro Kanda, Koji Tsuzaki,

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A case of bulbospinal muscular atrophy with large fasciculation manifesting as spinal myoclonus Manabu Inoue, Yasuhiro Kojima, Masutaro Kanda, Koji Tsuzaki, Yoko Shibata, Toshiaki Hamano, Hiroshi Shibasaki Clinical Neurophysiology Practice Volume 2, Pages 62-64 (January 2017) DOI: 10.1016/j.cnp.2017.01.001 Copyright © 2017 International Federation of Clinical Neurophysiology Terms and Conditions

Fig. 1 Surface EMG records of leg muscles during and after voluntary muscle contraction. Note the repetitive EMG discharges of small amplitude, corresponding to fasciculation (white arrow), in the gracilis muscles bilaterally during knee flexion and in the right vastus lateralis (Rt. VL) muscle during knee extension. Immediately following the end of the knee movement, EMG discharges of large amplitude appeared in the VL muscles bilaterally and in the left gracilis muscle and remained for a few seconds, which corresponded to myoclonus (black arrowhead). Clinical Neurophysiology Practice 2017 2, 62-64DOI: (10.1016/j.cnp.2017.01.001) Copyright © 2017 International Federation of Clinical Neurophysiology Terms and Conditions