Rasmussen syndrome: An Argentinean experience in 32 patients

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Rasmussen syndrome: An Argentinean experience in 32 patients Roberto H. Caraballo, Sebastian Fortini, Ricardo Cersósimo, Soledad Monges, María C. Pasteris, María Gomez, María Celeste Buompadre, Eduardo Monese, Carolina Vilte, Marcelo Bartuluchi  Seizure - European Journal of Epilepsy  Volume 22, Issue 5, Pages 360-367 (June 2013) DOI: 10.1016/j.seizure.2013.02.003 Copyright © 2013 British Epilepsy Association Terms and Conditions

Fig. 1 Background activity shows delta–theta slow waves in the right hemisphere. Seizure - European Journal of Epilepsy 2013 22, 360-367DOI: (10.1016/j.seizure.2013.02.003) Copyright © 2013 British Epilepsy Association Terms and Conditions

Fig. 2 Interictal EEG shows frequent slow waves and spike discharges in the right fronto-temporal regions. Seizure - European Journal of Epilepsy 2013 22, 360-367DOI: (10.1016/j.seizure.2013.02.003) Copyright © 2013 British Epilepsy Association Terms and Conditions

Fig. 3 Background activity shows slow theta waves and epileptiform discharges in the left hemisphere. Seizure - European Journal of Epilepsy 2013 22, 360-367DOI: (10.1016/j.seizure.2013.02.003) Copyright © 2013 British Epilepsy Association Terms and Conditions

Fig. 4 Interictal EEG recording shows synchronic and asymmetric bilateral spikes. Seizure - European Journal of Epilepsy 2013 22, 360-367DOI: (10.1016/j.seizure.2013.02.003) Copyright © 2013 British Epilepsy Association Terms and Conditions

Fig. 5 A and B normal T2-weighted images (TR/TE 5500/80ms) at onset (A) and 14 months later (B); note progressive atrophy of the left frontoparietal cortex and enlarged subarachnoid spaces. Seizure - European Journal of Epilepsy 2013 22, 360-367DOI: (10.1016/j.seizure.2013.02.003) Copyright © 2013 British Epilepsy Association Terms and Conditions

Fig. 6 A and B T2-weighted images (TR/TE 5500/80ms) showing normal axial slices at the level of the Silvian fissure in another patient at onset (A) and 24 months later (B); note asymmetric Silvian fissures with right enlarged subarachnoid spaces. Also see T2 prolongation and atrophy of the homolateral striatum. Seizure - European Journal of Epilepsy 2013 22, 360-367DOI: (10.1016/j.seizure.2013.02.003) Copyright © 2013 British Epilepsy Association Terms and Conditions