Neurofibromatosis Type 1 Associated With Moyamoya Syndrome in Children Anna Duat-Rodríguez, MD, Fernando Carceller Lechón, MD, Miguel Ángel López Pino, MD, Cristina Rodríguez Fernández, MD, Luis González-Gutiérrez-Solana, MD Pediatric Neurology Volume 50, Issue 1, Pages 96-98 (January 2014) DOI: 10.1016/j.pediatrneurol.2013.04.007 Copyright © 2014 Elsevier Inc. Terms and Conditions
Figure 1 Axial magnetic resonance angiography shows collapsed three-dimensional time-of-flight image with occlusion of both distal internal carotid arteries (arrows). Internal carotid arteries have a bilateral stenosis of the supraclinoid internal carotid artery and proximal anterior and middle cerebral arteries. Marked development of multiple collateral circulation (thalamus perforating and lenticulostriate arteries). Pediatric Neurology 2014 50, 96-98DOI: (10.1016/j.pediatrneurol.2013.04.007) Copyright © 2014 Elsevier Inc. Terms and Conditions
Figure 2 Axial fluid-attenuated inversion recovery magnetic resonance shows hyperintensity (arrows) in the sulci in the left frontal lobe. These bright sulci (leptomeningeal “ivy sign”) are due to slow-flowing engorged pial vessels and thickened arachnoid membranes. Pediatric Neurology 2014 50, 96-98DOI: (10.1016/j.pediatrneurol.2013.04.007) Copyright © 2014 Elsevier Inc. Terms and Conditions