AJKD Atlas of Renal Pathology: Nail-Patella Syndrome–Associated Nephropathy  Behzad Najafian, MD, Kelly Smith, MD, PhD, Mark A. Lusco, MD, Charles E. Alpers,

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AJKD Atlas of Renal Pathology: Nail-Patella Syndrome–Associated Nephropathy  Behzad Najafian, MD, Kelly Smith, MD, PhD, Mark A. Lusco, MD, Charles E. Alpers, MD, Agnes B. Fogo, MD  American Journal of Kidney Diseases  Volume 70, Issue 4, Pages e19-e20 (October 2017) DOI: 10.1053/j.ajkd.2017.08.001 Copyright © 2017 National Kidney Foundation, Inc. Terms and Conditions

Figure 1 Nail-patella–like renal disease (also known as LMX1B-associated nephropathy) with segmental glomerulosclerosis in a 39-year-old man with dystrophic nails, but no patellar or other skeletal abnormalities (Jones silver stain). American Journal of Kidney Diseases 2017 70, e19-e20DOI: (10.1053/j.ajkd.2017.08.001) Copyright © 2017 National Kidney Foundation, Inc. Terms and Conditions

Figure 2 Electron microscopy of nail-patella-like renal disease (also know as LMX1B-associated nephropathy) with scattered deposition of fibrillar collagen in glomerular basement membranes and mesangial matrix (arrows); inset: magnified view of collagen fibrils, some of which have curved appearance. American Journal of Kidney Diseases 2017 70, e19-e20DOI: (10.1053/j.ajkd.2017.08.001) Copyright © 2017 National Kidney Foundation, Inc. Terms and Conditions