Maturation of recoded cystic fibrosis transmembrane conductance regulator (CFTR) channels. a) Representative Western blot obtained from HEK293 cells expressing.

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Maturation of recoded cystic fibrosis transmembrane conductance regulator (CFTR) channels. a) Representative Western blot obtained from HEK293 cells expressing the indicated construct. Maturation of recoded cystic fibrosis transmembrane conductance regulator (CFTR) channels. a) Representative Western blot obtained from HEK293 cells expressing the indicated construct. CFTR bands C and B are indicated. b) CFTR maturation as measured using the C/(B+C) ratio under control conditions. #: significant difference compared with wild-type control conditions (p<0.01, ANOVA followed by a Fisher test). Iwona Pranke et al. ERJ Open Res 2018;4:00080-2017 ©2018 by European Respiratory Society