Multifocal motor neuropathy with conduction block.

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1 Copyright © 2014 Elsevier Inc. All rights reserved. Chapter 19 Diabetes and the Nervous System Douglas W. Zochodne and Cory Toth.
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Figure 3 3D magnetic resonance neurography
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Various lower limb ankle orthoses used in the management of distal lower limb muscle weakness in patients with inherited neuropathies. Various lower limb.
This patient (shown from behind) presented with slowly progressive weakness and wasting of the shoulder girdles, neurophysiological evidence of denervation.
(A) This 54 year old man with the flail arm syndrome has severe wasting of the arms causing profound weakness. (A) This 54 year old man with the flail.
 Extension lateral cervical spine radiograph showing normal alignment of the upper cervical spine.  Extension lateral cervical spine radiograph showing.
Plain CT scan of head (a) and prethrombectomy (b, c), during thrombectomy (d, e, f) and post-thrombectomy (g, h) digital subtraction angiogram images in.
TOS with C8 neuropathy. TOS with C8 neuropathy. A 17-year-old girl (trumpet player) with left arm and hand weakness in an ulnar distribution, exacerbated.
 (A, B).  (A, B). Median motor nerve conduction study. Active recording electrode is over the APB muscle, with stimulation at the wrist, elbow, axilla,
 These traces show typical electrophysiological features of a pre-synaptic neuromuscular transmission disorder in a patient with LEMS. The traces on the.
(A) Confocal image of a skin biopsy taken from the finger of a healthy subject illustrating different subtypes of sensory fibre: PGP 9.5 is used as an.
Typical MRI features of Creutzfeldt-Jakob disease (CJD).
The MR scan of brain of our case vignette patient showing significant occipital lobe atrophy (especially left sided) with parietal lobe involvement as.
Incidentalomas. Incidentalomas. T1W sagittal (A) and T2W coronal (B) MRIs show a small slightly T2 hypointense lesion (B, arrow) in the left anterior pituitary.
Multifocal motor neuropathy with conduction block.
Photograph of the legs of a patient with inherited erythromelalgia, showing erythema to the level of the mid-calf. Photograph of the legs of a patient.
MRI scans show coronal sections of the brain and right hippocampus at baseline, 9 months, 2 years (when he was diagnosed with mild cognitive impairment)
Plain CT scan of head (a) and prethrombectomy (b) and post-thrombectomy (c) digital subtraction angiograms in a 49-year-old woman with sudden onset left.
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Confocal images of skin biopsies taken from the legs of a control subject (A) and a patient with small fibre neuropathy secondary to HIV (B) showing PGP.
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This patient (shown from behind) presented with slowly progressive weakness and wasting of the shoulder girdles, neurophysiological evidence of denervation.
Photograph of the legs of a patient with inherited erythromelalgia, showing erythema to the level of the mid-calf. Photograph of the legs of a patient.
Confocal images of skin biopsies taken from the legs of a control subject (A) and a patient with small fibre neuropathy secondary to HIV (B) showing PGP.
Injection sites for greater occipital nerve (GON) block.
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Figure Spinal cord imaging (A, B) Sagittal and axial T2-weighted cervical spine MRI demonstrating hyperintensities in the central gray matter of patient.
Flexion cervical spine MRI in Hirayama disease showing expansion of the dural venous plexus with presumed chronic ischaemic damage preferentially involving.
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The person in (A) has spinal muscular atrophy type III and the person in (B) has Becker’s muscular dystrophy. The person in (A) has spinal muscular atrophy.
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Suggested algorithm of addressing non-motor symptoms in clinic (modified from Chaudhuri et al).48 HCP, healthcare professional; QoL, quality of life; PDSS,
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Constructive interference in the steady state (CISS) axial (A and B) and gadolinium-enhanced T1W axial (C and D) and coronal (E) MRI show a right-sided.
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The effect on finger arterial blood pressure of (A) standing in the crossed leg position with leg muscle contraction, (B) sitting on a derby chair, and.
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A patient with Cori-Forbes disease who had childhood hepatomegaly and hypoglycaemic episodes; despite a liver biopsy, there was no diagnosis. A patient.
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(A) High intensity lesions in the left dorsolateral midbrain on T2 weighted magnetic resonance imaging in case 1. (A) High intensity lesions in the left.
Dystonic tremor with writer’s cramp.
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[123I]-FP-CIT (DaTSCAN) images demonstrating: (top left) normal tracer uptake in the putamen and caudate nuclei; then progressively decreasing uptake in.
(A) Kinematic features of fast and accurate right wrist flexions performed by the patient before (left part) and after alcohol intake (right part). (A)
Kaplan-Meier table analysis of patients with corticobasal degeneration after onset of symptoms; the y axis refers to proportion of patients who are alive.
This 46-year-old man presented with a 20-year history of progressive distal wasting and weakness of the right hand and forearm muscles. This 46-year-old.
MR scan of brain fluid-attenuated inversion recovery (FLAIR) (A) and short tau inversion recovery (STIR) (B, C) showing asymmetrical hyperintensities affecting.
MR scans of brain and spine: (A) sagittal T2 image showing signal change in the posterior spinal cord between C3 and T6. MR scans of brain and spine: (A)
Patient number 20 with a left internal carotid artery dissection.
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(A) Clinical selection of scapular muscles depending on the side of the elevation of the shoulder in a patient with dystonic head rotation. (A) Clinical.
Axial T2-weighted MRI. (A and B) Dot-like hyperintensities characteristic of enlarged perivascular spaces (EPVS) in the basal ganglia in a patient with.
Figure MRI T1 coronal images show homogenous hyperintense lesion involving the right trigeminal nerve root (white arrows) in A and B and Meckel's cave.
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Multifocal motor neuropathy with conduction block. Multifocal motor neuropathy with conduction block. Hyperintense swollen right-sided nerve roots on cervical spine coronal MRI (left panel, modified with permission from71). It typically causes asymmetrical distal weakness, often involving finger extensors initially, but can progress to wasting and fixed flexion deformity, as in this patient, several years after symptom onset (right panel; for other images see72). Martin R Turner, and Kevin Talbot Pract Neurol doi:10.1136/practneurol-2013-000557 ©2013 by BMJ Publishing Group Ltd