Myocarditis af viral orsök

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Presentation transcript:

Myocarditis af viral orsök Dagur Ingi Jónsson 5.árs læknanemi

Skilgreining Myocarditis is a condition resulting from inflammation of the heart muscle. Myocellular damage results in myocardial dysfunction leading to heart failure

Orsakir myocarditis Infections Immune-related Annað Post-viral Veirur Parvovirus B19 Human Herpes Virus 6 Coxsackie A og B Influenza A og B CMV Adenoveirur Hepatitis B og C Bakteríur Snýkjudýr Sveppir Post-viral Post-streptococcal SLE Drug hypersensitivity Transplant rejection Annað System sjúkdómar Eituráhrif Lyf Toxin

Saga Tveir megin klínískir hópar Hratt vaxandi hjartabilun í kjölfar acute viremiu Hægt vaxandi hjartabilun án samfarandi sýkingar en söga um nýlega efri öndunarfærasýkingu eða gastroenteritis

Einkenni og teikn Flensulík einkenni Einkenni hjartabilunnar Yngri Respiratory distress mest áberandi Hjartahlustun S3 og S4 gallop Mitral/Tricuspid leki Lungnahlustun Vökvi basalt Yngri Slappleiki Vanþrif Pirringur Eldri Kvarta um slappleika Þreytast fljótt Brjóstverkur Andstutt

Greining Saga og skoðun EKG Blóðprufur - TroponinT Rgt lungu Hjartaómskoðun MRI Myocardial biopsy og PCR fyrir veirum EKG – óspecifískar breytingar Blóðprufur – CK og TroponinT er hærra sé skaði enn í gangi Rgt lungu – stækkað hjarta og stasamynd Hjartaómskoðun – víkkuð hólf og minnkaður samdráttur í sleglum Myocardial biopsy – veiruleit með PCR MRI - gadolinum

Pathophysiology 1. Veira ræðst á myocardial frumur Ósérhæft ónæmissvar 3. Bati eða framgangur í dilated cardiomyopathy

Meðferð Skv. Amerískum guidelines Meðferð vegna hjartabilunnar Önnur meðferð sem telst ósönnuð Sterar IVIG Interferon alfa Ribavirin

Framfarir í sjónmáli? Betri skilgreining á sjúkdómsferli – beita meðferð eftir hvar í sjúkdómsferli gripið er inn Anti-cytokine agents Náttúrulyf A. membranaceus A. chinensis Bólusetningar (Coxsackie B3)

Heimildir Allan. Clinical Manifestations and diagnosis of myocarditis in children. Uptodate.com. Júlí 2009. Allan. Treatment and prognosis of myocarditis in children. Uptodate.com. Janúar 2008. Brunetti, DeSantis. Treatment of viral myocarditis caused by coxsackievirus B. Clinical Consultation. Janúar 2008. Cooper. Etiology and pathogenesis of myocarditis. Uptodate.com. Júní 2009. Cooper. Myocarditis. N Eng J Med. Apríl 2009. Hay, Levin, Sondheimer, Deterding. Current Diagnosis and Treatment in Pediatrics. 18th edition. 2007. Lange Medical Books. Kumar, Cotran, Robbins. Basic Pathology. 7th edition. 2003. Saunders