Flecainide treats a novel KCNJ2 mutation associated with Andersen-Tawil syndrome Hanora A. Van Ert, BSN, Elise C. McCune, Kate M. Orland, MS, Kathleen.

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Presentation transcript:

Flecainide treats a novel KCNJ2 mutation associated with Andersen-Tawil syndrome Hanora A. Van Ert, BSN, Elise C. McCune, Kate M. Orland, MS, Kathleen R. Maginot, MD, Nicholas H. Von Bergen, MD, Craig T. January, MD, PhD, Lee L. Eckhardt, MD, FHRS HeartRhythm Case Reports Volume 3, Issue 2, Pages 151-154 (February 2017) DOI: 10.1016/j.hrcr.2016.11.009 Copyright © 2016 Heart Rhythm Society Terms and Conditions

Figure 1 Example traces from 48 hour Holter monitor example traces. A: Run of polymorphic ventricular tachycardia (VT) that develops features of bidirectional VT; B: bidirectional VT; C: sinus tachycardia suppresses ventricular ectopy; D: summary data. HeartRhythm Case Reports 2017 3, 151-154DOI: (10.1016/j.hrcr.2016.11.009) Copyright © 2016 Heart Rhythm Society Terms and Conditions

Figure 2 Resting electrocardiogram (ECG): A: ventricular bigeminy obscures QTc or QTu measurement; B: ECG on atenolol 12.5 mg twice daily (black arrows indicate postectopic U-wave accentuation); C: ECG on atenolol and flecainide (white arrows indicate U-wave). HeartRhythm Case Reports 2017 3, 151-154DOI: (10.1016/j.hrcr.2016.11.009) Copyright © 2016 Heart Rhythm Society Terms and Conditions