Marfan syndrome: The variability and outcome of operative management

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Presentation transcript:

Marfan syndrome: The variability and outcome of operative management Joseph S. Coselli, MD, Scott A. LeMaire, MD, Suat Büket, MD  Journal of Vascular Surgery  Volume 21, Issue 3, Pages 432-443 (March 1995) DOI: 10.1016/S0741-5214(95)70285-7 Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 1 A, Preoperative drawing and CT scan of patient with symptomatic AAA; patient had undergone prior TAAA replacement. B, Postoperative drawing and aortogram after AAA replacement. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 1 A, Preoperative drawing and CT scan of patient with symptomatic AAA; patient had undergone prior TAAA replacement. B, Postoperative drawing and aortogram after AAA replacement. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 2 A, Preoperative drawing and aortogram of patient with TAAA (Crawford, type I) caused by chronic DeBakey type III dissection; patient had previous CVG replacement. B, Postoperative drawing and aortogram after TAAA repair with reattachment of multiple intercostal arteries. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 2 A, Preoperative drawing and aortogram of patient with TAAA (Crawford, type I) caused by chronic DeBakey type III dissection; patient had previous CVG replacement. B, Postoperative drawing and aortogram after TAAA repair with reattachment of multiple intercostal arteries. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 3 A, Preoperative drawing and aortogram of patient with false aneurysm arising from site of right coronary artery reattachment on previously placed CVG (Bentall operation). B, Drawing and CT scan. C, Postoperative drawing and aortogram after repair, with Dacron graft to right coronary origin, and additional distal aortic graft inserted. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 3 A, Preoperative drawing and aortogram of patient with false aneurysm arising from site of right coronary artery reattachment on previously placed CVG (Bentall operation). B, Drawing and CT scan. C, Postoperative drawing and aortogram after repair, with Dacron graft to right coronary origin, and additional distal aortic graft inserted. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 3 A, Preoperative drawing and aortogram of patient with false aneurysm arising from site of right coronary artery reattachment on previously placed CVG (Bentall operation). B, Drawing and CT scan. C, Postoperative drawing and aortogram after repair, with Dacron graft to right coronary origin, and additional distal aortic graft inserted. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 4 A, Preoperative aortogram and drawing of patient with annuloaortic ectasia. B, Postoperative drawing and aortogram after CVG insertion with direct reattachment of coronary ostia via button technique. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 4 A, Preoperative aortogram and drawing of patient with annuloaortic ectasia. B, Postoperative drawing and aortogram after CVG insertion with direct reattachment of coronary ostia via button technique. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 5 A, Preoperative aortogram and drawing of patient with extensive TAAA (Crawford type II) caused by chronic DeBakey type III dissection. B, Postoperative aortogram and drawing of patient after TAAA replacement. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 5 A, Preoperative aortogram and drawing of patient with extensive TAAA (Crawford type II) caused by chronic DeBakey type III dissection. B, Postoperative aortogram and drawing of patient after TAAA replacement. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 6 A, Preoperative drawing and aortogram of patient with chronic DeBakey type III dissection and aneurysms of descending and thoracoabdominal aorta (Crawford type IV). B, Postoperative drawing and aortogram after separate replacement of descending aorta and thoracoabdominal aorta. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 6 A, Preoperative drawing and aortogram of patient with chronic DeBakey type III dissection and aneurysms of descending and thoracoabdominal aorta (Crawford type IV). B, Postoperative drawing and aortogram after separate replacement of descending aorta and thoracoabdominal aorta. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 7 A, Preoperative aortogram and drawing of patient with annuloaortic ectasia, aortic valvular insufficiency, and superimposed chronic DeBakey type II dissection. B, Drawing and CT scan of aneurysm with 12 cm diameter. C, Postoperative drawing and aortogram after CVG insertion with use of Cabrol technique. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 7 A, Preoperative aortogram and drawing of patient with annuloaortic ectasia, aortic valvular insufficiency, and superimposed chronic DeBakey type II dissection. B, Drawing and CT scan of aneurysm with 12 cm diameter. C, Postoperative drawing and aortogram after CVG insertion with use of Cabrol technique. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions

Fig. 7 A, Preoperative aortogram and drawing of patient with annuloaortic ectasia, aortic valvular insufficiency, and superimposed chronic DeBakey type II dissection. B, Drawing and CT scan of aneurysm with 12 cm diameter. C, Postoperative drawing and aortogram after CVG insertion with use of Cabrol technique. Journal of Vascular Surgery 1995 21, 432-443DOI: (10.1016/S0741-5214(95)70285-7) Copyright © 1995 Society for Vascular Surgery and International Society for Cardiovascular Surgery, North American Chapter Terms and Conditions