Cardiac outcome in classic infantile Pompe disease after 13 years of treatment with recombinant human acid alpha-glucosidase Carine I. van Capelle, Esther.

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Cardiac outcome in classic infantile Pompe disease after 13 years of treatment with recombinant human acid alpha-glucosidase Carine I. van Capelle, Esther Poelman, Ingrid M. Frohn-Mulder, Laurens P. Koopman, Johanna M.P. van den Hout, Luc Régal, Bjorn Cools, Wim A. Helbing, Ans T. van der Ploeg International Journal of Cardiology Volume 269, Pages 104-110 (October 2018) DOI: 10.1016/j.ijcard.2018.07.091 Copyright © 2018 The Authors Terms and Conditions

Fig. 1 Left ventricular cardiac dimensions over time. A) LVMI Z-scores B) LVPWd Z-scores C) LVMI raw scores D) LVM raw scores. Each of the 14 patients is represented by a different line. The dashed grey lines represent the upper and lower limit of normal (Z-score of +2 and −2) and normal value (Z-score of 0). International Journal of Cardiology 2018 269, 104-110DOI: (10.1016/j.ijcard.2018.07.091) Copyright © 2018 The Authors Terms and Conditions

Fig. 2 Echocardiographic parasternal long axis view of patient 9. Echocardiographic parasternal long axis view of patient 9 at A) baseline and B) after 5 years of treatment. Note the major difference in both septal and posterior wall thickness. International Journal of Cardiology 2018 269, 104-110DOI: (10.1016/j.ijcard.2018.07.091) Copyright © 2018 The Authors Terms and Conditions