Management and Outcomes of Heterotaxy Syndrome Associated With Pulmonary Atresia or Pulmonary Stenosis Vinod A. Sebastian, MD, Javier Brenes, MD, Raghav.

Slides:

Advertisements

Similar presentations

Ricardo L. Oliveira, MD, Moishe Liberman, MD, PhD

Advertisements

Results of Coronary Artery Endarterectomy and Coronary Artery Bypass Grafting for Diffuse Coronary Artery Disease Srikrishna Sirivella, MD, Isaac Gielchinsky,

Elizabeth A. David, MD, David T

Definitive or Preoperative Chemoradiation Therapy for Esophageal Cancer: Patterns of Care and Survival Outcomes Meng S. Shao, MD, Andrew T. Wong, MD,

Leiomyosarcoma of the Superior Vena Cava

Arterial Switch for Transposed Great Vessels With Intact Ventricular Septum Beyond One Month of Age Kai Ma, MD, PhD, Zhongdong Hua, MD, Keming Yang,

Chun Chieh Lin, PhD, MBA, Matthew P

Joshua E. Rosen, BASc, Hari B

Clinical Implications of Major Aortopulmonary Collateral Arteries in Patients With Right Isomerism Jui-Yu Hsu, MD, Jou-Kou Wang, MD, PhD, Ming-Tai Lin,

Hybrid Transcatheter-Surgical Strategy in Arterial Tortuosity Syndrome

Hancock II Bioprosthesis for Aortic Valve Replacement: The Gold Standard of Bioprosthetic Valves Durability? Tirone E. David, MD, Susan Armstrong, MS,

Elliot Wakeam, MD, MPH, Meredith Giuliani, MBBS, MEd, Natasha B

Clinical Profile and Natural History of 453 Nonsurgically Managed Patients With Severe Aortic Stenosis Padmini Varadarajan, MD, Nikhil Kapoor, MD, Ramesh.

Long-Term Consequences of Postoperative Heart Failure After Surgery for Aortic Stenosis Compared With Coronary Surgery Farkas B. Vánky, MD, PhD, Erik.

Bart P. Van Putte, MD, PhD, Tim Smith, MD, PhD, Thom L

Early Outcomes of Primary Sutureless Repair of the Pulmonary Veins

Michael E. Halkos, MD, Patrick Kilgo, MS, Omar M

Initial Experience With Hybrid Palliation for Neonates With Single-Ventricle Physiology Christopher A. Caldarone, MD, Lee Benson, MD, Helen Holtby, MD,

Robert E. Merritt, MD, Richard I. Whyte, MD, Nicole T

Influence of Pulmonary Hypertension on Patients With Idiopathic Pulmonary Fibrosis Awaiting Lung Transplantation Don Hayes, MD, MS, Sylvester M. Black,

Eric M. Graham, MD, Sinai C. Zyblewski, MD, Jacob W

Bidirectional Cavopulmonary Shunt in Patients With Anomalies of Systemic and Pulmonary Venous Drainage Doff B McElhinney, MS, V.Mohan Reddy, MD, Phillip.

Single Ostium of the Right and Left Coronary Artery From the Right Pulmonary Artery Katarzyna Januszewska, MD, PhD, Hans-Gerd Kehl, MD, PhD, Edward Malec,

Biventricular Repair for Right Atrial Isomerism

Risk Factors for Mortality After the Norwood Procedure Using Right Ventricle to Pulmonary Artery Shunt Shunji Sano, MD, Shu-Chien Huang, MD, Shingo Kasahara,

Lymph Node Evaluation Achieved by Open Lobectomy Compared With Thoracoscopic Lobectomy for N0 Lung Cancer Robert E. Merritt, MD, Chuong D. Hoang, MD,

Anomalous Great Cardiac Vein Draining Into the Superior Vena Cava

Aortic Valve Replacement Improves Survival in Severe Aortic Stenosis Associated With Severe Pulmonary Hypertension Ramdas G. Pai, MD, Padmini Varadarajan,

Bahaaldin Alsoufi, MD, Sally Cai, PhD, Glen S

Association of Thoracic Aorta Calcium Score With Left Ventricular Hypertrophy and Clinical Outcomes in Patients With Severe Aortic Stenosis After Aortic.

Risk Factors of Neurologic Deficit After Thoracic Aortic Endografting

Total Arterial Revascularization: A Superior Strategy for Diabetic Patients Who Require Coronary Surgery James Tatoulis, MD, FRACS, Rochelle Wynne, PhD,

Ricardo L. Oliveira, MD, Moishe Liberman, MD, PhD

James D. St. Louis, MD The Annals of Thoracic Surgery

Yong Wang, MD, Xiaomei Zheng, MD, Kexiang Liu, PhD

Fontan Pathway Growth: A Quantitative Evaluation of Lateral Tunnel and Extracardiac Cavopulmonary Connections Using Serial Cardiac Magnetic Resonance

Age-Dependent Gender Disparities in Post Lung Transplant Survival Among Patients With Idiopathic Pulmonary Fibrosis Shahid I. Sheikh, MD, Don Hayes,

Analysis of Surgical Outcome in Complex Double-Outlet Right Ventricle With Heterotaxy Syndrome or Complete Atrioventricular Canal Defect Koh Takeuchi,

Use of Amiodarone After Major Lung Resection

Elliot Wakeam, MD, MPH, James P. Byrne, MD, Gail E

Ritu Sachdeva, MD, Richard T. Fiser, MD, William R

Anomalous Origin of Left Pulmonary Artery From Left Subclavian Artery

Felix G. Fernandez, MD, Onkar Khullar, MD, Seth D

Hemodynamic Assessment After Complete Repair of Pulmonary Atresia With Major Aortopulmonary Collaterals Richard D. Mainwaring, MD, V. Mohan Reddy, MD,

Muhammad Aanish Raees, MBBS, Driss Mazhar, DFGSM, Jason T

Aorto-Left Ventricular Tunnel: An Alternative Surgical Approach

Takashi Murashita, MD, Kevin L. Greason, MD, Rakesh M

Adriaan W. Schneider, MD, Nico A. Blom, MD, PhD, Eline F

Posttransplant Outcomes Among Septuagenarians Bridged to Transplantation With Continuous-Flow Left Ventricular Assist Devices Shinichi Fukuhara, MD,

Mohammad A. Zafar, MBBS, Emily A

Pretransplant Panel Reactive Antibodies in Human Lung Transplantation: An Analysis of Over 10,000 Patients Ashish S. Shah, MD, Lois Nwakanma, MD, Christopher.

Late results of palliative atrial switch for transposition, ventricular septal defect, and pulmonary vascular obstructive disease Harold M Burkhart,

Brian M. Cardis, MD, Derek A. Fyfe, MD, PhD, William T. Mahle, MD

Tracheal Reconstruction in the Pediatric Population: How I Teach It

Contemporary Outcomes of Surgical Repair of Total Anomalous Pulmonary Venous Connection in Patients With Heterotaxy Syndrome Muhammad S. Khan, MD, Roosevelt.

Cardiac Surgery in Select Nonagenarians: Should We or Shouldn’t We?

Left Ventricular Reconstruction Benefits Patients With Dilated Ischemic Cardiomyopathy Atsushi Yamaguchi, MD, Hideo Adachi, MD, Koji Kawahito, MD, Seiichiro.

Invited Commentary The Annals of Thoracic Surgery

Hypoplastic Left Heart Syndrome With Anomalous Origin of the Right Coronary Artery Julie Cleuziou, MD, Felix Haas, MD, Christian Schreiber, MD, Hans-Jörg.

Superior Vena Cava to Pulmonary Artery Anastomosis as an Adjunct to Biventricular Repair: 38-Year Follow-Up Siho Kim, MD, Osman Al-Radi, MD, Mark K.

Repair of Truncus Arteriosus and Aortic Arch Interruption: Outcome Analysis Takashi Miyamoto, MD, Nicodème Sinzobahamvya, MD, Daiva Kumpikaite, MD, Boulos.

Cardiac Myxomas: A 50-Year Experience With Resection and Analysis of Risk Factors for Recurrence Ishan K. Shah, MD, Joseph A. Dearani, MD, Richard C.

Performing the Left Atrial Maze Ablation Pattern Without Atriotomy

Total Anomalous Pulmonary Venous Connection: An Analysis of Current Management Strategies in a Single Institution Camille L. Hancock Friesen, MD, David.

Clinical Outcome After Pulmonary Resection for Lung Cancer Patients on Hemodialysis Toshiro Obuchi, MD, Wakako Hamanaka, MD, Yasuhiro Yoshida, MD, Jun.

Yangfeng Tang, MD, Zilin Liao, MD, Lin Han, MD, Zhiyun Xu, MD

Wilson Y. Szeto, MD, Joseph E. Bavaria, MD, Frank W

Esophagectomy for T1 Esophageal Cancer: Outcomes in 100 Patients and Implications for Endoscopic Therapy Arjun Pennathur, MD, Andrew Farkas, BA, Alyssa.

Ascending Aortic Extension for Enlargement of the Aortopulmonary Space in Children with Pulmonary Artery Stenosis Craig J. Baker, MD, Winfield J. Wells,

Surgical Reconstruction of Peripheral Pulmonary Arteries: Strategies, Outcomes, and New Classification Abdulaziz Al-Khaldi, MD, MS, Omar Tamimi, MD

Presentation transcript:

Management and Outcomes of Heterotaxy Syndrome Associated With Pulmonary Atresia or Pulmonary Stenosis Vinod A. Sebastian, MD, Javier Brenes, MD, Raghav Murthy, MD, Surendranath Veeram Reddy, MD, V. Vivian Dimas, MD, Alan Nugent, MBBS, Thomas Zellers, MD, Rong Huang, MS, Kristine J. Guleserian, MD, Joseph M. Forbess, MD The Annals of Thoracic Surgery Volume 98, Issue 1, Pages 159-166 (July 2014) DOI: 10.1016/j.athoracsur.2014.02.076 Copyright © 2014 The Society of Thoracic Surgeons Terms and Conditions

Fig 1 Algorithm for management of heterotaxy with pulmonary atresia/pulmonary stenosis. (TAPVR = total anomalous pulmonary venous return.) The Annals of Thoracic Surgery 2014 98, 159-166DOI: (10.1016/j.athoracsur.2014.02.076) Copyright © 2014 The Society of Thoracic Surgeons Terms and Conditions

Fig 2 Clinical management of heterotaxy with pulmonary atresia/pulmonary stenosis. (TAPVR = total anomalous pulmonary venous return.) The Annals of Thoracic Surgery 2014 98, 159-166DOI: (10.1016/j.athoracsur.2014.02.076) Copyright © 2014 The Society of Thoracic Surgeons Terms and Conditions

Fig 3 Kaplan-Meier survival curve (blue line) is shown with the 95% confidence limits (range bars), with circles indicating censored patients. The Annals of Thoracic Surgery 2014 98, 159-166DOI: (10.1016/j.athoracsur.2014.02.076) Copyright © 2014 The Society of Thoracic Surgeons Terms and Conditions

Fig 4 Survival comparison is shown between heterotaxy patients with pulmonary atresia/pulmonary stenosis with total anomalous pulmonary venous return (TAPVR; dashed red line; red circles indicating censored patients) and those without TAPVR (solid blue line, blue circles indicating censored patients). Log-rank test showed significantly worsened survival in the TAPVR group (p = 0.038). The range bars show the 95% confidence limits. The Annals of Thoracic Surgery 2014 98, 159-166DOI: (10.1016/j.athoracsur.2014.02.076) Copyright © 2014 The Society of Thoracic Surgeons Terms and Conditions

Fig 5 Survival comparison is shown between heterotaxy patients with pulmonary atresia (PA)/pulmonary stenosis (PS) with total anomalous pulmonary venous return (TAPVR) who underwent operations at less than 30 days of age (solid red line; red circles indicating censored patients) vs the remaining patients in the cohort (dashed blue line, blue circles indicating censored patients). The log-rank test showed significant difference in survival between the two groups (p = 0.001). The range bars show the 95% confidence limits. The Annals of Thoracic Surgery 2014 98, 159-166DOI: (10.1016/j.athoracsur.2014.02.076) Copyright © 2014 The Society of Thoracic Surgeons Terms and Conditions

Fig 6 Drawing shows a patient with a left aortic arch and bilaterally discontinuous pulmonary arteries (PAs). (Ao = aorta; RA = right atrium; RPA = right pulmonary artery; RV = right ventricle; SVC = superior vena cava.) The Annals of Thoracic Surgery 2014 98, 159-166DOI: (10.1016/j.athoracsur.2014.02.076) Copyright © 2014 The Society of Thoracic Surgeons Terms and Conditions

Fig 7 Surgical reconstruction is shown in a patient with left aortic arch and bilaterally discontinuous pulmonary arteries. After ductal resection, the right subclavian artery and left carotid artery are used to reconstruct right and left pulmonary artery respectively. The Annals of Thoracic Surgery 2014 98, 159-166DOI: (10.1016/j.athoracsur.2014.02.076) Copyright © 2014 The Society of Thoracic Surgeons Terms and Conditions

Fig 8 Drawing shows patient with right aortic arch and bilaterally discontinuous pulmonary arteries. (LPA = left pulmonary artery; RPA = right pulmonary artery.) The Annals of Thoracic Surgery 2014 98, 159-166DOI: (10.1016/j.athoracsur.2014.02.076) Copyright © 2014 The Society of Thoracic Surgeons Terms and Conditions

Fig 9 Surgical reconstruction is shown in a patient with a right aortic arch and bilaterally discontinuous pulmonary arteries. After ductal resection, the right carotid artery and left subclavian artery are used to reconstruct right and left pulmonary artery respectively. The Annals of Thoracic Surgery 2014 98, 159-166DOI: (10.1016/j.athoracsur.2014.02.076) Copyright © 2014 The Society of Thoracic Surgeons Terms and Conditions