Patient case study 2—fibrotic uILD in the setting of IPAF

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Coinvolgimento polmonare nella sclerosi sistemica Marco Matucci Cerinic Departments of Rheumatology AVC BioMedicine & Division of Rheumatology AOUC Medicine,

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Presentation transcript:

Patient case study 2—fibrotic uILD in the setting of IPAF Patient case study 2—fibrotic uILD in the setting of IPAF. CTD, connective tissue disease; DLco, diffusing capacity of the lung for carbon monoxide; FVC, forced vital capacity; HRCT, high-resolution CT; ILD, interstitial lung disease; IPAF, interstitial pne... Patient case study 2—fibrotic uILD in the setting of IPAF. CTD, connective tissue disease; DLco, diffusing capacity of the lung for carbon monoxide; FVC, forced vital capacity; HRCT, high-resolution CT; ILD, interstitial lung disease; IPAF, interstitial pneumonia with autoimmune features; IPF, idiopathic pulmonary fibrosis; MDT, multidisciplinary team; uILD, unclassifiable interstitial lung disease; UIP, usual interstitial pneumonia. Toby M Maher et al. BMJ Open Resp Res 2018;5:e000289 ©2018 by British Thoracic Society