Unclassifiable interstitial fibrosis.

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Presentation transcript:

Unclassifiable interstitial fibrosis. Unclassifiable interstitial fibrosis. This low power view shows patchy fibrosis with focal microscopic honeycombing, airspace enlargement, scattered lymphoid aggregates, and central nonspecific interstitial pneumonia fibrosis-like changes. Further clinical history for this 49-year-old woman with early greying of hair and a sibling with pulmonary fibrosis suggested the likely diagnosis was familial interstitial pulmonary fibrosis. Scale bar=2 mm. Kirk D. Jones Eur Respir Rev 2018;27:170132 ©2018 by European Respiratory Society