Long-term follow-up of permanent atrial standstill in a German family with mutation in the SCN5A gene H. Immo Lehmann, MD, Ulf Meltendorf, MD, Helmut.

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Long-term follow-up of permanent atrial standstill in a German family with mutation in the SCN5A gene H. Immo Lehmann, MD, Ulf Meltendorf, MD, Helmut U. Klein, MD, PhD, FHRS HeartRhythm Case Reports Volume 4, Issue 8, Pages 356-358 (August 2018) DOI: 10.1016/j.hrcr.2018.04.015 Copyright © 2018 Heart Rhythm Society Terms and Conditions

Figure 1 Partial pedigree of the family. Empty symbols indicate phenotypically unaffected members (circles indicate females, squares indicate males), and filled symbols depict members with permanent atrial standstill. + indicates genotype positive; − indicates genotype negative; asterisk indicates no genotyping performed. HeartRhythm Case Reports 2018 4, 356-358DOI: (10.1016/j.hrcr.2018.04.015) Copyright © 2018 Heart Rhythm Society Terms and Conditions

Figure 2 Electrocardiogram of Patient III-2 (50 mm/s). No P waves could be detected—even in lead V1—consistent with complete persistent atrial standstill. HeartRhythm Case Reports 2018 4, 356-358DOI: (10.1016/j.hrcr.2018.04.015) Copyright © 2018 Heart Rhythm Society Terms and Conditions