Early Surgical Experience With Loeys-Dietz: A New Syndrome of Aggressive Thoracic Aortic Aneurysm Disease Jason A. Williams, MD, Bart L. Loeys, MD, Lois.

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Early Surgical Experience With Loeys-Dietz: A New Syndrome of Aggressive Thoracic Aortic Aneurysm Disease Jason A. Williams, MD, Bart L. Loeys, MD, Lois U. Nwakanma, MD, Harry C. Dietz, MD, Philip J. Spevak, MD, Nishant D. Patel, BA, Katrien François, MD, Julie DeBacker, MD, Vincent L. Gott, MD, Luca A. Vricella, MD, Duke E. Cameron, MD The Annals of Thoracic Surgery Volume 83, Issue 2, Pages S757-S763 (February 2007) DOI: 10.1016/j.athoracsur.2006.10.091 Copyright © 2007 The Society of Thoracic Surgeons Terms and Conditions

Fig 1 This photograph of a young boy with Loeys-Dietz syndrome demonstrates the characteristic feature of hypertelorism that occurs in 90% of patients with this disorder. The Annals of Thoracic Surgery 2007 83, S757-S763DOI: (10.1016/j.athoracsur.2006.10.091) Copyright © 2007 The Society of Thoracic Surgeons Terms and Conditions

Fig 2 (A) Indications for surgery in 21 patients with Loeys-Dietz syndrome undergoing surgical repair. (B) Aortic operations in 21 patients with Loeys-Dietz syndrome.*Both patients had undergone prior aortic root replacement at outside institutions. (VSRR = valve-sparing root replacement.) The Annals of Thoracic Surgery 2007 83, S757-S763DOI: (10.1016/j.athoracsur.2006.10.091) Copyright © 2007 The Society of Thoracic Surgeons Terms and Conditions