Aortic and Mitral Valve Involvement in Maroteaux-Lamy Syndrome VI: Surgical Implications in the Enzyme Replacement Therapy Era Salvatore Torre, MD, Mauro Scarpelli, MD, PhD, Alessandro Salviati, MD, PhD, Ebba Buffone, MD, Giuseppe Faggian, MD, Giovanni Battista Luciani, MD The Annals of Thoracic Surgery Volume 102, Issue 1, Pages e23-e25 (July 2016) DOI: 10.1016/j.athoracsur.2015.11.062 Copyright © 2016 The Society of Thoracic Surgeons Terms and Conditions
Fig 1 Intraoperative view of aortic valve showing thickening and retraction of the three valve leaflets. The Annals of Thoracic Surgery 2016 102, e23-e25DOI: (10.1016/j.athoracsur.2015.11.062) Copyright © 2016 The Society of Thoracic Surgeons Terms and Conditions
Fig 2 Electronic microscopic images showing pleiomorphic inclusions, including zebra bodies, membranous cytoplasmic bodies, and dense core inclusions at ×20,000 (A) and ×50,000 (B), typical of mucopolysaccharidosis. The Annals of Thoracic Surgery 2016 102, e23-e25DOI: (10.1016/j.athoracsur.2015.11.062) Copyright © 2016 The Society of Thoracic Surgeons Terms and Conditions