MRI in autosomal recessive hereditary spastic paraplegia: high T2 signal intensity in periventricular white matter and corona radiata with thin corpus.

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Figure 1 . Brain MRI (T1 axial image post gadolinium) showing mass-like heterogeneous enhancement involving the right caudate nucleus.
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Figure 1. MRI features of AP5Z1-associated complicated spastic paraplegia MRI features of AP5Z1-associated complicated spastic paraplegia (A) Periventricular.
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Figure 1 Family pedigree and MRI
Diffusion-weighted (TR = 3900, TE = 94, B = 1000, number of gradient directions = 90) imaging (A) with corresponding apparent diffusion coefficient map.
Susceptibility-weighted MRI of ex vivo hippocampal tissue.
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 Axial MRI of a 46 year old man with secondary progressive MS showing a large left sided periventricular lesion which is hyperintense with (A) T2 weighted.
1, Axial T2 image in patient 1 demonstrates bilateral cystic spaces in the biparietal periventricular white matter. 2, Axial T2 image in patient 2 demonstrating.
Ultrasonography (A–C) and MR imaging (D and E) (time interval, 7 days) from an infant with NKHG.A–C, Sagittal views showing (A) a hypoplastic corpus callosum.
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MRI. MRI. (A1–A2) Patient 6 with simple PNH, (B1–B2) patient 10 with plus PNH. (A1) Sagittal TSE T2 WI shows multiple periventricular nodules (arrows).
Case 1: Axial DWI through the maxillary sinus level demonstrates high signal intensity within the affected left maxillary sinus (black asterisk) compared.
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Axial T1-weighted MRI of the thigh (A) and lower leg (B) for case 1 shows fatty infiltration of the quadriceps and adductor muscles (L2, 3 and 4 myotomes;
MR scans of brain and spine: (A) sagittal T2 image showing signal change in the posterior spinal cord between C3 and T6. MR scans of brain and spine: (A)
A–C, Axial T2-weighted images 7 days after the ictus, demonstrating punctate hyperintensities throughout the white matter, on a background of slightly.
Axial DWIs at the level of the corona radiata obtained at 2 different time points (A and B) show recurrent periventricular infarcts. Axial DWIs at the.
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Isolated restricted diffusion in a patient who recovered without residual symptoms.A, DW image shows asymmetric (right greater than left) high signal intensity.
Scatterplot of the log of infarct signal intensity on DW images versus the log of hours from symptom onset. Scatterplot of the log of infarct signal intensity.
Marked progression of PML documented by serial MR studies
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MRI in autosomal recessive hereditary spastic paraplegia: high T2 signal intensity in periventricular white matter and corona radiata with thin corpus callosum. MRI in autosomal recessive hereditary spastic paraplegia: high T2 signal intensity in periventricular white matter and corona radiata with thin corpus callosum. Reprinted with permission from Hourani R, et al. Am J Neuroradiol 2009;30(5):936–40. DOI: https://doi.org/10.3174/ajnr.A1483. Lina Nashef et al. Pract Neurol 2019;19:115-130 ©2019 by BMJ Publishing Group Ltd