a) A 2-year-old male with Niemann–Pick disease type A

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Presentation transcript:

a) A 2-year-old male with Niemann–Pick disease type A a) A 2-year-old male with Niemann–Pick disease type A. Chest radiograph shows multiple airspace consolidations in right lower and middle lobes, and diffuse reticulonodular infiltrate. b) A 7-year-old male with Niemann–Pick disease type C and NPC2 mutation. a) A 2-year-old male with Niemann–Pick disease type A. Chest radiograph shows multiple airspace consolidations in right lower and middle lobes, and diffuse reticulonodular infiltrate. b) A 7-year-old male with Niemann–Pick disease type C and NPC2 mutation. High-resolution computed tomography shows bilateral patchy airspace ground-glass opacities with diffuse thickening of the interlobular septa. Francesca Santamaria et al. Eur Respir Rev 2013;22:437-453 ©2013 by European Respiratory Society