Abdominal magnetic resonance imaging of a patient with tuberous sclerosis complex lymphangioleiomyomatosis and multiple small renal angiomyolipomas (arrows) in T1-weighted images (a) and fat suppression signal sequences (b). Abdominal magnetic resonance imaging of a patient with tuberous sclerosis complex lymphangioleiomyomatosis and multiple small renal angiomyolipomas (arrows) in T1-weighted images (a) and fat suppression signal sequences (b). Left nephrectomy was performed for a large angiomyolipoma. S. Harari et al. Eur Respir Rev 2011;20:034-044 ©2011 by European Respiratory Society