CONGENITAL AORTIC DISEASE
EMBRYOLOGY HYPOTHETICAL DOUBLE AORTIC ARCH (Edward JE)
NORMAL LEFT AORTIC ARCH DEVELOPMENT
AORTIC ANOMALIES
AORTIC ARCH ANOMALIES RIGHT ARCH DOUBLE ARCH CERVICAL ARCH COARCTATION INTERRUPTED AORTIC ARCH PSEUDOCOARCTATION ABERRANT RIGHT SUBCLAVIAN ARTERY PATENT DUCTUS ARTERIOSIS
AORTIC ARCH ANOMALIES PRESENTATION VASCULAR RING –STRIDOR, WHEEZE, INFECTION, DYSPHAGIA ASSOCIATED CARDIAC DISORDERS –CYANOSIS, CONGESTIVE HEART FAILURE
RIGHT AORTIC ARCH MOST COMMON TYPES MIRROR IMAGE ABERRANT LEFT SUBCLAVIAN ISOLATED LEFT SUBCLAVIAN
MIRROR IMAGE RIGHT AORTIC ARCH
MIRROR IMAGE RIGHT AORTIC ARCH DEVELOPMENT
MIRROR IMAGE RIGHT AORITIC ARCH IN ASYMPTOMATIC ADULT
MIRROR IMAGE RIGHT AORTIC ARCH CYANOTIC HEART DISEASE IN 98% TETRALOGY, TRUNCUS, TRANSPOSITION,TRICUSPID ATRESIA RARE... VASCULAR RING & NO HEART DEFECT INDENTS RIGHT SIDE OF TRACHEA & ESOPHAGUS
ABERRANT LEFT SUBCLAVIAN RIGHT AORTIC ARCH
ABERRANT LEFT SUBCLAVIAN RIGHT AORTIC ARCH DEVELOPMENT
ABERRANT LEFT SUBCLAVIAN RIGHT AORTIC ARCH ASYMPTOMATIC ADULT
AB LEFT SUBCLAVIAN RIGHT ARCH ANEURYSM OF LEFT SUBCLAVIAN ARTERY
ABERRANT LEFT SUBCLAVIAN RIGHT AORTIC ARCH MOST COMMON RIGHT ARCH RARELY CAUSES SYMPTOMS RARELY FORMS A VASCULAR RING THAT AFFECTS ESOPH, TRACHEA DIVERTICULUM OF KOMMERELL INDENTS POSTERIOR ESOPHAGUS
ISOLATED LEFT SUBCLAVIAN RIGHT AORTIC ARCH
ISOLATED LEFT SUBCLAVIAN RIGHT AORTIC ARCH DEVELOPMENT
ISOLATED LEFT SUBCLAVIAN ARTERY RIGHT AORTIC ARCH SIGNS AND SYMPTOMS OF LEFT ARM ISCHEMIA
ISOLATED LEFT SUBCLAVIAN RIGHT AORTIC ARCH RARE CAUSE OF ARM ISCHEMIA –DECREASED PULSE, FATIGUE, DISCOMFORT SUBCLAVIAN STEAL SYNDROME
DOUBLE AORTIC ARCH
DOUBLE AORTIC ARCH DEVELOPMENT
DOUBLE AORTIC ARCH CHILD WITH RECURRENT PNEUMONIA
DOUBLE AORTIC ARCH CHILD WITH DYSPHAGIA
64-YEAR-OLD WOMAN BROUGHT TO ER AFTER MVA
ASYMPTOMATIC ADULT
DOUBLE AORTIC ARCH MOST COMMON COMPLETE VASCULAR RING STRIDOR, WHEEZE, INFECTION, DYSPHAGIA CONGENITAL HEART DISEASE IS RARE INDENTATION OF BOTH SIDES ESOPHAGUS
CERVICAL AORTIC ARCH
RIGHT AORTIC ARCH LEFT AORTIC ARCH
CERVICAL AORTIC ARCH
CERVICAL ARCH RIGHT SUBCLAVIAN FROM DIVERTICULUM
RIGHT CERVICAL ARCH ABERRANT LEFT SUBCLAVIAN ARTERY
CERVICAL AORTIC ARCH OFTEN NO SYMPTOMS TRACHEAL OR ESOPHAGEAL COMPRESSION WHEEZING, STRIDOR, COUGHING CHOKING, RECURRENT PNEUMONIA PALPABLE SUPRACLAVICULAR MASS CONGENITAL HEART DISEASE TEF, VSD, PDA COARCTATION OF DESCENDING AORTA
COARCTATION
5% OF CONGENITAL HEART DISEASE POSTDUCTAL ADULT TYPE COARCTATION DISTAL TO DUCTUS OR LIGAMENTUM ARTERIOSUM JUXTADUCTAL INFANTS AND CHILDREN HYPOPLASIA OF TRANSVERSE AORTIC ARCH AND AORTIC ISTHMUS. DUCTUS AT AREA OF COARCTATION AORTIC ARCH INTERRUPTION 95% HAVE PDA, 50% HAVE VSD
COARCTATION AORTIC KNOB FIGURE 3 AORTIC KNOB DILATED ARTERIES COLLATERALS ARTERIES LEFT SUBCLAVIAN ARTERY ASCENDING AORTA RIB NOTCHING LEFT VENTRICLE HYPERTROPHY ENLARGEMENT
FIGURE 3 AORTIC KNOB PRE AND POST STENOTIC DILATION
COARCTATION “FIGURE 3” AORTA KNOB
COLLATERAL VESSELS
COARCTATION
COARCTATION LEFT VENTRICULAR ENLARGEMENT
CHEST RADIOGRAPH DILATED LEFT SUBCLAVIAN ARTERY
RIB NOTCHING
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34-YEAR-OLD MAN AUTOMOBILE ACCIDENT
COARCTATION AORTIC VALVE –MAJORITY DEFORMED OR BICUSPID 10% HAVE CEREBRAL ANEURYMS AORTIC DISSECTION CHD HEART DISEASE COMMON ASSOCIATED ANOMALIES –TURNER SYNDROME,
HEMOPTYSIS 10 YEARS POST COARC REPAIR AORTOBRONCHIAL FISTULA
COARCTATION VERSUS PSEUDOCOARCTATION
PSEUDOCOARCTATION
KINK AT INSERTION SITE OF LIGAMENTUM ARTERIOSUM MINIMAL GRADIENT ACROSS DEFORMITY
PSEUDOCOARCTATION ARCH BUCKLED AT LIG. ARTERIOSUM
PSEUDOCOARCTATION MOST OFTEN DISCOVERED AS A MEDIASTINAL MASS ON PA CHEST RADIOGRAPH LOOK FOR KINK OF DESCENDING AORTA ON LATERAL CHEST RADIOGRAPH MEASUREMENT OF GRADIENT ACROSS KINK MAY BE NECESSARY TO DIFFERENTIATE FROM COARCTATION
ABERRANT RIGHT SUBCLAVIAN ARTERY
ABERRANT RIGHT SUBCLAVIAN ARTERY DEVELOPMEN T
ABERRANT RIGHT SUBCLAVIAN ARTERY
MOST COMMON ARTERIAL ANOMALY IN CHEST ALMOST ALWAYS AN INCIDENTAL FINDING OBLIQUE INDENTATION, POSTERIOR ESOPHAGUS CAN OCCUR WITH OTHER ANOMALIES
ABERRANT RIGHT SUBCLAVIAN ART AORTIC DISSECTION
LIGAMENTUM ARTERIOSUM
BOVINE AORTIC ARCH
THE END
PATENT DUCTUS ARTERIOSIS