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OSTEOCHONDROMA Cartilage capped exostosis
Commonest benign tumour of bone Metaphyseal developmental abnormality D FRANTZEN OSTEOCHONDROMA
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INCIDENCE 45 % of benign bony tumours 12 % of all bony tumours
Become evident < 20 yrs Solitary or multiple Any enchondral ossification bone D FRANTZEN OSTEOCHONDROMA
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CLINICALLY Lump or mechanical problem Tendon or nerve irritation
Sessile or pedunculated 50% distal femur, proximal tibia, proximal humerus D FRANTZEN OSTEOCHONDROMA
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CLINICAL Active growth during puberty
Move towards diaphysis during growth Excise if troublesome in second decade D FRANTZEN OSTEOCHONDROMA
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RADIOLOGY Flat/ sessile / pedunculated Tumour blending into metaphysis
Pedunculated orientated proximally Cartilage cap with calcification D FRANTZEN OSTEOCHONDROMA
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PATHOLOGY Normal bone covered by normal cartilage cap
Cartilage cap resembles normal growth plate Cartilage more disorganized D FRANTZEN OSTEOCHONDROMA
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PATHOLOGY Covered by thin layer of periosteum
Binucleate chondrocytes in lacunae D FRANTZEN OSTEOCHONDROMA
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TREATMENT Nil required unless symptomatic
Extra-capsular marginal excision Recurrence < 5% D FRANTZEN OSTEOCHONDROMA
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PROGNOSIS Risk of malignancy if solitary - 0.2 %
Risk of malignancy in diaphyseal aclasia : - 20 % Sarcomatous changes usually low- grade D FRANTZEN OSTEOCHONDROMA
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