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Crystal structure of human short/branched chain acyl-CoA dehydrogenase (PDB file 2JIF). A homotetramer with bound butyryl-Co as substrate is represented.

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Presentation on theme: "Crystal structure of human short/branched chain acyl-CoA dehydrogenase (PDB file 2JIF). A homotetramer with bound butyryl-Co as substrate is represented."— Presentation transcript:

1 Crystal structure of human short/branched chain acyl-CoA dehydrogenase (PDB file 2JIF). A homotetramer with bound butyryl-Co as substrate is represented. Note the high level of homology with the structure for isovaleryl-CoA dehydrogenase (Fig. 93-3). Structural motifs are represented as in Fig The image was generated by WebLab Viewer Pro software, v 4.0 (Molecular Simulations Inc.). Source: Branched Chain Organic Acidurias, The Online Metabolic and Molecular Bases of Inherited Disease Citation: Valle D, Beaudet AL, Vogelstein B, Kinzler KW, Antonarakis SE, Ballabio A, Gibson K, Mitchell G. The Online Metabolic and Molecular Bases of Inherited Disease; 2014 Available at: Accessed: October 23, 2017 Copyright © 2017 McGraw-Hill Education. All rights reserved

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