1. Pseudoxanthoma elasticum This is a generalized condition in which elastic fibers are degenerative. Clinical signs of the phenomenon can be recognized in the skin and eyes. In the skin, patches of yellowish discoloration and general laxness or redundancy develop on the neck (“chicken skin”), in the axillae, and in other places, such as the fossae of limbs and the inguinal folds, where considerable movement of skin is normal. In the eye, angioid streaks can be seen. They represent the result of faulty elastic fibers in Bruch membrane and generally precede the cutaneous changes. These eye changes frequently result in the loss of central vision and sometimes result in almost complete blindness. Peripheral vision is maintained.
Source: Genodermatoses, Weinberg's Color Atlas of Pediatric Dermatology, 5e
Citation: Prose NS, Kristal L. Weinberg's Color Atlas of Pediatric Dermatology, 5e; 2017 Available at: Accessed: November 12, 2017
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