1. IDIOPATHIC BIG BLIND SPOT SYNDROME AND ACUTE ZONAL OCCULT OUTER RETINOPATHY (AZOOR)
Gölge Acaroğlu, Yasemin Özdamar,
Özlem Aslan, Seyhan S. Özkan
S.B Ankara Ulucanlar Eye Hospital

2. Case Report: 29 y.o. F, Slowly proggressive visual loss over 2 years.
VA:0.8 (OD), 0.5 (OS)
Color vision full (OU)
Equal, reactive pupils, no RAPD
Anterior segment / vitreus normal
Brain / orbit MRI normal
CSF pressure normal
Systemic / neurological work-up normal.

3. Fundi: Bilateral discedema, mild temporal optic atrophy (OS), retina and vessels normal. FA: Leakage on the optic nerve heads.

4. Automated Static Visual Fields: Bilateral big blind spots.

5. Multifocal ERG: Bilateral macular depression.

6. Conclusion:
Presumed diagnosis of AZOOR was made and patient received immune supressive therapy. Symptoms and signs are improving.
Idiopathic big blind spot syndrome and retinal white dot syndromes are thought to be related to each other and their co- existance is termed as Acute Zonal Occult Outer Retinopathy (AZOOR).
AZOOR is a rare presumed autoimmune degeneration of outer retinal layers. It should be kept in mind in the differential diagnosis of young, otherwise healthy patients with papilledema and optic nerve dysfunction.