1. Expanding the electrical phenotype of NKX2-5 mutations: Ventricular tachycardia, atrial fibrillation, and complete heart block within one family 
Simone Jhaveri, MD, Peter F. Aziz, MD, FHRS, Elizabeth Saarel, MD, FHRS 
HeartRhythm Case Reports 
Volume 4, Issue 11, Pages (November 2018)
DOI: /j.hrcr
Copyright © 2018 Heart Rhythm Society Terms and Conditions

2. Figure 1
Pacemaker device interrogation for patient 1 showing atrial flutter at a cycle length of 160 ms, persistent despite antitachycardia pacing (arrow).
HeartRhythm Case Reports 2018 4, DOI: ( /j.hrcr )
Copyright © 2018 Heart Rhythm Society Terms and Conditions

3. Figure 2
Progression of atrioventricular (AV) nodal disease in patient 2. A: Electrocardiogram (ECG) at 17 years showing sinus bradycardia and first-degree AV block with PR interval of 400 ms. B: ECG at 18 years showing complete heart block with AV dissociation and a narrow complex escape rhythm.
HeartRhythm Case Reports 2018 4, DOI: ( /j.hrcr )
Copyright © 2018 Heart Rhythm Society Terms and Conditions

4. Figure 3
Holter monitor for patient 2 demonstrating a run of ventricular tachycardia at 180 beats/min.
HeartRhythm Case Reports 2018 4, DOI: ( /j.hrcr )
Copyright © 2018 Heart Rhythm Society Terms and Conditions

5. Supplemental Figure
Pacemaker device interrogation for patient 2. A: Demonstrating an episode of atrial fibrillation/flutter at a cycle length of 120 ms. B: Demonstrating 3.1% of total time in atrial tachycardia.
HeartRhythm Case Reports 2018 4, DOI: ( /j.hrcr )
Copyright © 2018 Heart Rhythm Society Terms and Conditions