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BENAZIR BHUTTO HOSPITAL
ENT DEPARTMENT BENAZIR BHUTTO HOSPITAL
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KARTAGENER SYNDROME 1904 Siewert described triad Situs inversus Chronic Sinusitis & Bronchiectasis 1933 Mane’s Kartagener recognized this syndrom Situs inversus , Chronic Sinusitis, Bronchiectasis is inherited via autosomal recessive Symptoms results from Defective cilia motility Normal motile cilia are responsible Clearance of mucus membrane with regular, fast and synchronous beating pattern dust viruses bacteria are illuminated
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UPPER RESPIRATORY TRACT
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Upper Respiratory Tract
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“The united airways concept”
Kartagener Syndrome
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KARTAGENER SYNDROME (E.N.T. PROBLEMS)
Recurrent Upper respiratory tract infections Rhinosinusitis Otitis media with effusion Acute otitis media Chronic otitis media General morbidity Temporary relieved by repeated antibiotics Surgical intervention needed myringotomy + gromet & FESS
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RHINOSINUSITIS Chronic, Thick, Mucoid Rhinorea from early childhood
Pale, swollen nasal mucosa, Mucoprulent secretion, impaired sense of smell Nasal polyps 30% Sinus pressure headache Symptoms improve with antibiotic therapy Recurrence common
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Otitis media
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OTITIS MEDIA Common menifestation Otitis media with effusion
Acute Otitis Media Chronic Otitis Media Tympanosclerosis Cholesteatoma
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Ear Infection
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QUALITY OF LIFE IS IMPROVED BY
EARLY RECOGNITION MEDICAL MANAGEMENT NASAL DOUCHING REPEATED ANTIBIOTICS ANTI-ALERGIC SURGICAL TREATMENT MYRINGOTOMY TUBE F.E.S.S.
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THANKYOU
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