1. Probable Adult Polyglucosan Body Disease
Caroline M. Klein, MD, PhD, E. Peter Bosch, MD, Peter J. Dyck, MD 
Mayo Clinic Proceedings 
Volume 75, Issue 12, Pages (December 2000)
DOI: /
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2. Fig. 1
T2-weighted magnetic resonance images. A, Axial image demonstrates hyperintense confluent white matter lesions in periventricular frontal and occipital regions. B, Sagittal image shows prominent cervical spinal cord atrophy.
Mayo Clinic Proceedings  , DOI: ( / )
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3. Fig. 2
Suralnervebiopsyspecimens revealedprominent large polyglucosan bodies. A, Longitudinal paraffin-embedded section stained withLuxolfast blue/periodic acid-Schiff demonstrates an enlarged polyglucosan body separating the myelin sheath of a myelinated fiber (arrow). B, Semithin epoxy-embedded cross section of a largepolyglucosan bodystainedwithmethylene blue surrounded by thinned myelin(arrow). C, Transmission electron micrograph of a typical polyglucosan bodydemonstrating a separation between the edge of the polyglucosan body and normalappearing axoplasm (arrow). Note the overlapping fibrilsembedded withina densebackground matrixmaterial.
Mayo Clinic Proceedings  , DOI: ( / )
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