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Changes of CFTR functional measurements and clinical improvements in cystic fibrosis patients with non p.Gly551Asp gating mutations treated with ivacaftor 

Published by谓齐 巴 Modified over 5 years ago

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Presentation on theme: "Changes of CFTR functional measurements and clinical improvements in cystic fibrosis patients with non p.Gly551Asp gating mutations treated with ivacaftor "— Presentation transcript:

1 Changes of CFTR functional measurements and clinical improvements in cystic fibrosis patients with non p.Gly551Asp gating mutations treated with ivacaftor  Myriam Mesbahi, Michal Shteinberg, Michael Wilschanski, Aurelie Hatton, Thao Nguyen–Khoa, Hannah Friedman, Michael Cohen, Virginie Escabasse, Muriel Le Bourgeois, Vicenzina Lucidi, Isabelle Sermet-Gaudelus, Laurence Bassinet, Galit Livnat  Journal of Cystic Fibrosis  Volume 16, Issue 1, Pages (January 2017) DOI: /j.jcf Copyright © Terms and Conditions

2 Fig. 1 Regression graph between absolute change in FEV1 (% predicted) and change in NPD score (e(Δ Cl−free Isoproterenol/Δ Amiloride)). Journal of Cystic Fibrosis  , 45-48DOI: ( /j.jcf ) Copyright © Terms and Conditions

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