1. Bilateral cochlear nerve absence in a 7-year-old patient with severe dysplasia and bilateral absence of the cochlea (patient C10).
Bilateral cochlear nerve absence in a 7-year-old patient with severe dysplasia and bilateral absence of the cochlea (patient C10). Facial nerve function was preserved.A, Axial T2-weighted fast spin-echo MR image of the left side shows dysplasia of the vestibule and semicircular canals (arrow). Cochlea was absent.B, Oblique sagittal MR image obtained on the same side shows a small IAC containing only two nerves. The intact facial nerve lies anteriorly (arrowhead). We suspected that the posterior nerve was vestibular, on the basis of its position and the absence of cochlear structures (arrow).
Christine M. Glastonbury et al. AJNR Am J Neuroradiol 2002;23:
©2002 by American Society of Neuroradiology