1. BOR syndrome.
BOR syndrome. A, Axial CT image through the level of the cochlear aperture demonstrates a hypoplastic cochlea without a definable modiolus or apical turn. B, An image slightly superior to A demonstrates a medially displaced canal for the labyrinthine segment of the facial nerve (arrow) and an enlarged vestibular aqueduct. This patient also has a left middle ear cholesteatoma causing ossicular erosion. Only the head of the malleus remains (arrowhead in A). C, CT image through the right epitympanum in the same patient demonstrates a foreshortened dysplastic incus with an enlarged body that essentially articulates directly with the stapes.
B.Y. Huang et al. AJNR Am J Neuroradiol 2012;33:
©2012 by American Society of Neuroradiology