1. Innovation and excellence in health and care Addenbrooke’s Hospital I Rosie Hospital The Nurse Experience EWGGD, Paris 2012 Liz Morris UK

2. Innovation and excellence in health and care Disclaimers Fees for speaking/travel grants received from Genzyme and Shire

3. Innovation and excellence in health and care Nursing: UK origins Origins in the 19 th century Unskilled helpers Florence Nightingale 1860

4. Nursing: today “To help people sick or well in the performance of those activities contributing to health or its recovery …that they would perform unaided if they had the necessary strength will or knowledge…. to help people gain independence as rapidly as possible” Virginia Henderson 1966 Innovation and excellence in health and care

5. Nursing : Gaucher disease Innovation and excellence in health and care

6. Nursing: roles Innovation and excellence in health and care

7. Nursing: Enzyme Replacement Therapy (ERT) Innovation and excellence in health and care Zimran A, Hollak C et al Home treatment with intravenous enzyme replacement therapy for Gaucher disease: an international collaborative study of 33 patients Blood vol82, no 4 (August15), 1993:pp110--1109

8. Nursing: home ERT schemes Providers Hospital Community Industry Innovation and excellence in health and care Work in preparation by C E M Hollak et al data from 2008

9. Nursing: equipment Innovation and excellence in health and care

10. Nursing: venous access Nursing packages Nurse administration Training patient/carer Cannulation only On call Innovation and excellence in health and care

12. Nursing: equipment Innovation and excellence in health and care

13. Nursing: home therapy safety Home ERT >20 years experience (182 patients) 4 reported AE’s – allergic responses, 1 severe Central venous access device (CVAD)complications - 2 patients port-a- cath central sepsis (both splenectomised) - 3 blocked ports Innovation and excellence in health and care

14. Thank you Innovation and excellence in health and care

15. Nursing: the patient Innovation and excellence in health and care