Presentation is loading. Please wait.

Presentation is loading. Please wait.

Crystal structure of human branched-chain α-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease.

Published byWhitney Atkins Modified over 9 years ago

Similar presentations

Presentation on theme: "Crystal structure of human branched-chain α-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease."— Presentation transcript:

1 Crystal structure of human branched-chain α-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease Arnthor Ævarsson, Jacinta L Chuang, R Max Wynn, Stewart Turley, David T Chuang, Wim GJ Hol Structure Volume 8, Issue 3, Pages 277-291 (March 2000) DOI: 10.1016/S0969-2126(00)00105-2

2 Figure 1 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

3 Figure 2 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

4 Figure 3 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

5 Figure 4 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

6 Figure 5 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

7 Figure 6 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

8 Figure 7 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

9 Figure 8 Structure 2000 8, 277-291DOI: (10.1016/S0969-2126(00)00105-2)

Download ppt "Crystal structure of human branched-chain α-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease."

Similar presentations

Structure of a Ubiquitin E1-E2 Complex: Insights to E1-E2 Thioester Transfer Shaun K. Olsen, Christopher D. Lima Molecular Cell Volume 49, Issue 5, Pages.

Structure of a Ubiquitin E1-E2 Complex: Insights to E1-E2 Thioester Transfer Shaun K. Olsen, Christopher D. Lima Molecular Cell Volume 49, Issue 5, Pages.
Individualized Medicine from Prewomb to Tomb Eric J. Topol Cell Volume 157, Issue 1, Pages 241-253 (March 2014) DOI: 10.1016/j.cell.2014.02.012 Copyright.

Individualized Medicine from Prewomb to Tomb Eric J. Topol Cell Volume 157, Issue 1, Pages (March 2014) DOI: /j.cell Copyright.
Eph-Ephrin Bidirectional Signaling in Physiology and Disease Elena B. Pasquale Cell Volume 133, Issue 1, Pages 38-52 (April 2008) DOI: 10.1016/j.cell.2008.03.011.

Eph-Ephrin Bidirectional Signaling in Physiology and Disease Elena B. Pasquale Cell Volume 133, Issue 1, Pages (April 2008) DOI: /j.cell
Crystal structure of mammalian purple acid phosphatase Luke W Guddat, Alan S McAlpine, David Hume, Susan Hamilton, John de Jersey, Jennifer L Martin Structure.

Crystal structure of mammalian purple acid phosphatase Luke W Guddat, Alan S McAlpine, David Hume, Susan Hamilton, John de Jersey, Jennifer L Martin Structure.
Connexin Mutations in Skin Disease and Hearing Loss David P. Kelsell, Wei-Li Di, Mark J. Houseman The American Journal of Human Genetics Volume 68, Issue.

Connexin Mutations in Skin Disease and Hearing Loss David P. Kelsell, Wei-Li Di, Mark J. Houseman The American Journal of Human Genetics Volume 68, Issue.
Molecular Model of a Cell Plasma Membrane With an Asymmetric Multicomponent Composition: Water Permeation and Ion Effects Robert Vácha, Max L. Berkowitz,

Molecular Model of a Cell Plasma Membrane With an Asymmetric Multicomponent Composition: Water Permeation and Ion Effects Robert Vácha, Max L. Berkowitz,
Functional Analysis of the Neurofibromatosis Type 2 Protein by Means of Disease- Causing Point Mutations Renee P. Stokowski, David R. Cox The American.

Functional Analysis of the Neurofibromatosis Type 2 Protein by Means of Disease- Causing Point Mutations Renee P. Stokowski, David R. Cox The American.
Gene Preference in Maple Syrup Urine Disease Mary M. Nellis, Dean J. Danner The American Journal of Human Genetics Volume 68, Issue 1, Pages 232-237 (January.

Gene Preference in Maple Syrup Urine Disease Mary M. Nellis, Dean J. Danner The American Journal of Human Genetics Volume 68, Issue 1, Pages (January.
The Molecular Basis of Focal Cyst Formation in Human Autosomal Dominant Polycystic Kidney Disease Type I Feng Qian, Terry J Watnick, Luiz F Onuchic, Gregory.

The Molecular Basis of Focal Cyst Formation in Human Autosomal Dominant Polycystic Kidney Disease Type I Feng Qian, Terry J Watnick, Luiz F Onuchic, Gregory.
Nuclear Receptors, RXR, and the Big Bang Ronald M. Evans, David J. Mangelsdorf Cell Volume 157, Issue 1, Pages 255-266 (March 2014) DOI: 10.1016/j.cell.2014.03.012.

Nuclear Receptors, RXR, and the Big Bang Ronald M. Evans, David J. Mangelsdorf Cell Volume 157, Issue 1, Pages (March 2014) DOI: /j.cell
Molecular Motors in Neurons: Transport Mechanisms and Roles in Brain Function, Development, and Disease Nobutaka Hirokawa, Shinsuke Niwa, Yosuke Tanaka.

Molecular Motors in Neurons: Transport Mechanisms and Roles in Brain Function, Development, and Disease Nobutaka Hirokawa, Shinsuke Niwa, Yosuke Tanaka.
Structure and Activity of Strigolactones: New Plant Hormones with a Rich Future Binne Zwanenburg, Tomáš Pospíšil Molecular Plant Volume 6, Issue 1, Pages.

Structure and Activity of Strigolactones: New Plant Hormones with a Rich Future Binne Zwanenburg, Tomáš Pospíšil Molecular Plant Volume 6, Issue 1, Pages.
Mesoscale Simulation of Blood Flow in Small Vessels Prosenjit Bagchi Biophysical Journal Volume 92, Issue 6, Pages 1858-1877 (March 2007) DOI: 10.1529/biophysj.106.095042.

Mesoscale Simulation of Blood Flow in Small Vessels Prosenjit Bagchi Biophysical Journal Volume 92, Issue 6, Pages (March 2007) DOI: /biophysj
Maple Syrup Urine Disease: Identification and Carrier-Frequency Determination of a Novel Founder Mutation in the Ashkenazi Jewish Population Lisa Edelmann,

Maple Syrup Urine Disease: Identification and Carrier-Frequency Determination of a Novel Founder Mutation in the Ashkenazi Jewish Population Lisa Edelmann,
The Mitochondrial Basis of Aging Nuo Sun, Richard J. Youle, Toren Finkel Molecular Cell Volume 61, Issue 5, Pages 654-666 (March 2016) DOI: 10.1016/j.molcel.2016.01.028.

The Mitochondrial Basis of Aging Nuo Sun, Richard J. Youle, Toren Finkel Molecular Cell Volume 61, Issue 5, Pages (March 2016) DOI: /j.molcel
Epidemiological trends and the effect of airport fever screening on prevention of domestic dengue fever outbreaks in Taiwan, 1998–2007 Mei-Mei Kuan, Ting.

Epidemiological trends and the effect of airport fever screening on prevention of domestic dengue fever outbreaks in Taiwan, 1998–2007 Mei-Mei Kuan, Ting.
Codon usage limitation in the expression of HIV-1 envelope glycoprotein Jürgen Haas, Eun-Chung Park, Brian Seed Current Biology Volume 6, Issue 3, Pages.

Codon usage limitation in the expression of HIV-1 envelope glycoprotein Jürgen Haas, Eun-Chung Park, Brian Seed Current Biology Volume 6, Issue 3, Pages.
2015 Alzheimer's disease facts and figures Alzheimer's & Dementia: The Journal of the Alzheimer's Association Volume 11, Issue 3, Pages 332-384 (March.

2015 Alzheimer's disease facts and figures Alzheimer's & Dementia: The Journal of the Alzheimer's Association Volume 11, Issue 3, Pages (March.
Genetic testing for high-risk colon cancer patients1 William M. Grady Gastroenterology Volume 124, Issue 6, Pages 1574-1594 (May 2003) DOI: 10.1016/S0016-5085(03)00376-7.

Genetic testing for high-risk colon cancer patients1 William M. Grady Gastroenterology Volume 124, Issue 6, Pages (May 2003) DOI: /S (03)
Nonspanning Bivalent Ligands as Improved Surface Receptor Binding Inhibitors of the Cholera Toxin B Pentamer Jason C. Pickens, Daniel D. Mitchell, Jiyun.

Nonspanning Bivalent Ligands as Improved Surface Receptor Binding Inhibitors of the Cholera Toxin B Pentamer Jason C. Pickens, Daniel D. Mitchell, Jiyun.

Similar presentations

Ads by Google